POLG1, C10ORF2, and ANT1 mutations are uncommon in sporadic progressive external ophthalmoplegia with multiple mitochondrial DNA deletions

G. Hudson, M. Deschauer, R. W. Taylor, M. G. Hanna, D. Fialho, A. M. Schaefer, L. P. He, E. Blakely, D. M. Turnbull, P. F. Chinnery

Research output: Contribution to journalArticlepeer-review

26 Scopus citations

Abstract

The authors sequenced POLG1, C10ORF2, and ANT1 in 38 sporadic progressive external ophthalmoplegia patients with multiple mitochondrial DNA (mtDNA) deletions. Causative mutations were identified in approximately10% of cases, with two unrelated individuals harboring a novel premature stop codon mutation (1356T>G). None had a mutation in C10ORF2 or ANT1. In the majority of patients, the primary nuclear genetic defect is likely to affect other unknown genes important for mtDNA maintenance.

Original languageEnglish
Pages (from-to)1439-1441
Number of pages3
JournalNeurology
Volume66
Issue number9
DOIs
StatePublished - May 2006
Externally publishedYes

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