Abstract
The first pathoanatomic case report of mucocutaneous lymph-node syndrome (MCLS) from Austria is presented. A 3 1/2 yr old boy was admitted to the Pediatric Department with a six day history of fever and bilateral conjunctivitis. He showed a maculous exanthema, red and fissuring lips, reddened tonsils and a coated tongue. Submandibular lymphnodes were swollen (1 cm diameter); ESR 128/138; peripheral leukocytosis 17 x 109/l. On the tenth day of illness, membranous desquamation from the fingertips and a strawberry tongue was observed. The ECG showed a myocardial infarction in the apical portion of the left ventricle. The boy died on the 25th day of illness. Pathological findings were found predominantly in the heart: coronary arteries showed fibrous thickening of intimal layer, focal destruction of elastic membranes and aneurysms in both arteries. The aneurysm in the descending branch of the left coronary artery was 15 mm long and had a maximum diameter of 8 mm. It was completely occluded by a thrombus, a recurring anteroseptal myocardial infarction. Other investigated arteries were not affected. Tonsils, as well as (paratracheal and parapancreatic) lymph-nodes, showed a few ceroid pigment containing histiocytes.
| Translated title of the contribution | Mucocutaneous lymph node syndrome in Austria. Three surviving and a lethal case. II: Pathological findings |
|---|---|
| Original language | German |
| Pages (from-to) | 318-321 |
| Number of pages | 4 |
| Journal | Klinische Padiatrie |
| Volume | 193 |
| Issue number | 4 |
| DOIs | |
| State | Published - 1981 |
| Externally published | Yes |