How should I treat an adult with unoperated complex cyanotic heart disease with severe pulmonary stenosis?

Bert Nagel; Robert Maier; Harald Kaemmerer; Martin Koestenberger; Andreas Gamillscheg; John Hess

doi:10.4244/EIJV10I2A48

How should I treat an adult with unoperated complex cyanotic heart disease with severe pulmonary stenosis?

Bert Nagel, Robert Maier, Harald Kaemmerer, Martin Koestenberger, Andreas Gamillscheg, John Hess

Clinic for Paediatric Cardiology

Research output: Contribution to journal › Article › peer-review

Abstract

BACKGROUND: A 33-year-old adult with complex congenital heart disease and severe cyanosis presented to us with increasing symptoms of hyperviscosity, decreasing exercise tolerance and a thromboembolic complication. INVESTIGATION: Physical examination, laboratory investigations, ECG, transthoracic echocardiogram, cardiopulmonary exercise testing, angiography. DIAGNOSIS: Subvalvular and valvular pulmonary stenosis due to a calcified pulmonary valve. TREATMENT: Amiodarone, angiotensin-converting enzyme inhibitor, beta-blockers, percutaneous pulmonary balloon valvuloplasty, warfarin.

Original language	English
Pages (from-to)	289-290+3p
Journal	EuroIntervention
Volume	10
Issue number	2
DOIs	https://doi.org/10.4244/EIJV10I2A48
State	Published - Jun 2014

Keywords

Congenital heart disease
Cyanosis
Palliation
Pulmonary valvuloplasty

Access to Document

10.4244/EIJV10I2A48

Cite this

@article{5eac057814cf48d79a918a0d97a5d76c,

title = "How should I treat an adult with unoperated complex cyanotic heart disease with severe pulmonary stenosis?",

abstract = "BACKGROUND: A 33-year-old adult with complex congenital heart disease and severe cyanosis presented to us with increasing symptoms of hyperviscosity, decreasing exercise tolerance and a thromboembolic complication. INVESTIGATION: Physical examination, laboratory investigations, ECG, transthoracic echocardiogram, cardiopulmonary exercise testing, angiography. DIAGNOSIS: Subvalvular and valvular pulmonary stenosis due to a calcified pulmonary valve. TREATMENT: Amiodarone, angiotensin-converting enzyme inhibitor, beta-blockers, percutaneous pulmonary balloon valvuloplasty, warfarin.",

keywords = "Congenital heart disease, Cyanosis, Palliation, Pulmonary valvuloplasty",

author = "Bert Nagel and Robert Maier and Harald Kaemmerer and Martin Koestenberger and Andreas Gamillscheg and John Hess",

year = "2014",

month = jun,

doi = "10.4244/EIJV10I2A48",

language = "English",

volume = "10",

pages = "289--290+3p",

journal = "EuroIntervention",

issn = "1774-024X",