TY - JOUR
T1 - Aorticopulmonary Paraganglioma With Severe Obstruction of the Pulmonary Artery
T2 - Successful Combined Treatment by Stenting and Surgery
AU - Qedra, Naser
AU - Kadry, Mahdi
AU - Buz, Semih
AU - Meyer, Rudolf
AU - Ewert, Peter
AU - Hetzer, Roland
PY - 2009/4
Y1 - 2009/4
N2 - Aorticopulmonary paraganglioma is a rare tumor of the middle mediastinum. Complete surgical resection is the only effective treatment, even when it may pose a surgical challenge due to the proximity of the tumor to the heart and great vessels, often rendering complete resection difficult to achieve. We report the case of a 30-year-old woman with an aorticopulmonary paraganglioma who presented with severe pulmonary hypertension due to obstruction of the pulmonary artery. In the first step, stenting of the pulmonary artery was performed and 2 months later a radical resection of the tumor using cardiopulmonary bypass under circulatory arrest and deep hypothermia was carried out. In addition, the ascending aorta and aortic arch were replaced by a prosthesis. The patient is in optimal condition and has now been disease-free for almost 7 years. We believe that this is the first description in the English literature of a successful combined management strategy in view of such an unusual manifestation of aorticopulmonary paraganglioma.
AB - Aorticopulmonary paraganglioma is a rare tumor of the middle mediastinum. Complete surgical resection is the only effective treatment, even when it may pose a surgical challenge due to the proximity of the tumor to the heart and great vessels, often rendering complete resection difficult to achieve. We report the case of a 30-year-old woman with an aorticopulmonary paraganglioma who presented with severe pulmonary hypertension due to obstruction of the pulmonary artery. In the first step, stenting of the pulmonary artery was performed and 2 months later a radical resection of the tumor using cardiopulmonary bypass under circulatory arrest and deep hypothermia was carried out. In addition, the ascending aorta and aortic arch were replaced by a prosthesis. The patient is in optimal condition and has now been disease-free for almost 7 years. We believe that this is the first description in the English literature of a successful combined management strategy in view of such an unusual manifestation of aorticopulmonary paraganglioma.
UR - http://www.scopus.com/inward/record.url?scp=62649162447&partnerID=8YFLogxK
U2 - 10.1016/j.athoracsur.2008.08.048
DO - 10.1016/j.athoracsur.2008.08.048
M3 - Article
C2 - 19324176
AN - SCOPUS:62649162447
SN - 0003-4975
VL - 87
SP - 1284
EP - 1286
JO - Annals of Thoracic Surgery
JF - Annals of Thoracic Surgery
IS - 4
ER -