An atypical right ventricle-dependent coronary circulation in a child with pulmonary artery stenosis

Nabil Tahhan, Lucile Houyel, Jerome Petit, Jurgen Horer, Sebastien Hascoet

Research output: Contribution to journalArticlepeer-review

Abstract

Right ventricle-dependent coronary circulation (RVDCC) is associated with pulmonary valve atresia and intact ventricular septum (PA-IVS). Currently, the suggested mechanism of coronary artery fistulas in PA-IVS is a primary anomaly of RV development, leading to progressive pulmonary atresia and development of abnormal fistulous communications between coronary arteries and the right ventricular cavity. We report the first case of RVDCC in a child with main pulmonary artery stenosis and normal RV development.

Original languageEnglish
Pages (from-to)74-76
Number of pages3
JournalProgress in Pediatric Cardiology
Volume49
DOIs
StatePublished - Jun 2018
Externally publishedYes

Keywords

  • Coronary artery fistula
  • Pulmonary artery stenosis
  • Right ventricle development
  • Right ventricle-dependent coronary circulation

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